Gross motor function classification system in patients with mucopolysaccharidosis.

sification system for individuals with MPS. However, the progression of motor function impairment such as walking, sitting, and functional independence in day to day activities is directly related to the severity of the disorder1,2,3. The “Gross Motor Function Classification System” (GMFCS) was developed to describe the severity of motor function impairment in patients with cerebral palsy4. This scale is stable for patients between the ages of 2 and 12, and its validity and reliability have given it international acceptance and use4,5. Such as in cerebral palsy, patients with MPS show motor function impairment that is associated with progressive joint stiffness and upper motor neuron injury. The GMFCS could also be used as a scale for systematic grading of MPS. This will allow for normalization of the functional motor severity in these subjects, enabling Gross Motor Function classiFication systeM in Patients with MucoPolysaccharidosis. SiStema de ClaSifiCaCiòn de la funCión motora en paCienteS Con muCopoliSaCaridoSiS. Marcos Almeida Matos1, Rosa Barreto2, Vitor Quadros1, Carlos Eduardo Penha1, Angelina Xavier Acosta2